(hairy cell leukemia HCL,有毛細胞性白血病)
→☆lymphocytes with cotoplasmic projections
TRAP(tartrate-resistant acid phosphatase)(bone turnover marker)
Causes marrow fibrosis → ☆dry tap on aspiration.
☆LUQ pain, massive splenomegaly, pancytopenia
cladribine(antimetabolites, ☆ADA inhibitor)
☆ADA converts adenosine/deoxyadenosine into inosine/deoxyinosine
→ inhibition of ADA activates alternate pathyway, leading to lymphocyte apoptosis
hematology
UWorld
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